CASE REPORT
A ocorrência de ependimomas infratentoriais extraventriculares em pacientes adultos é uma forma rara de tumor do sistema nervoso central. Relata-se o caso de um paciente masculino, 31 anos, previamente hígido, com quadro progressivo de vertigem, cefaleia, náuseas e vômitos. A neuroimagem evidenciou lesão expansiva no vérmis cerebelar, com obstrução do IV ventrículo por compressão e hidrocefalia associada. O paciente foi submetido à ressecção cirúrgica total da lesão e o diagnóstico de ependimoma grau 3 foi confirmado por análise histopatológica e imuno-histoquímica. A literatura ressalta a raridade dessa localização e a importância de um diagnóstico diferencial minucioso com outras neoplasias da fossa posterior. A ressecção completa precoce permanece fundamental para o controle tumoral e melhora do prognóstico.
Extraventricular infratentorial ependymomas in adults are rare central nervous system tumors. We report the case of a 31-year-old man who presented with progressive vertigo, headache, nausea, and vomiting. Neuroimaging revealed an expansive lesion in the cerebellar vermis, accompanied by compression and obstruction of the IV ventricle. The patient underwent a procedure in which the tumor was completely removed. The diagnosis of grade 3 ependymoma was confirmed by histopathological and immunohistochemical methods. The literature underscores the rarity of this location and the necessity of a meticulous differential diagnosis with other neoplasms of the posterior fossa. Early complete resection remains essential for tumor control and improved prognosis.
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1Serviço de Neurocirurgia do Hospital Cristo Redentor, Grupo Hospitalar Conceição, Porto Alegre, RS, Brasil.
2Universidade de Caxias do Sul, Caxias do Sul, RS, Brasil.
Received Jul 13, 2025
Accepted Aug 11, 2025
